Problems of diagnosis and treatment of chronic thromboembolic pulmonary hypertension
https://doi.org/10.17238/PmJ1609-1175.2017.4.6-16
Abstract
Chronic thromboembolic pulmonary hypertension (CTEPH) is a precapillary form of pulmonary hypertension in which chronic obstruction of large/ middle pulmonary arteries and secondary changes in the microcirculatory bed of the lungs lead to a progressive increase in pulmonary vascular resistance and pulmonary artery pressure followed by the development of severe right heart failure. CTEPH is a unique form of pulmonary hypertension, because it is potentially treatable with surgical treatment. This review presents the main statements of the national guidelines on the diagnosis and treatment of CTEPH 2015, addresses the problematic issues associated with the tasks of early diagnosis and effective treatment such as pulmonary trombendarterectomy, rational supportive and specific therapy, balloon angioplasty of the pulmonary arteries and lung/ heartlung complex transplantation. Algorithms for diagnosing and managing CTEPH patients are also proposed as the requirements for an expert center for CTEPH.
About the Authors
I. E. Chazova
National medical research center of cardiology
Russian Federation
Russian Federation
T. V. Martynyuk
National medical research center of cardiology
Russian Federation
Russian Federation
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Review
For citations:
Chazova I.E., Martynyuk T.V. Problems of diagnosis and treatment of chronic thromboembolic pulmonary hypertension. Pacific Medical Journal. 2017;(4):6-16. (In Russ.) https://doi.org/10.17238/PmJ1609-1175.2017.4.6-16
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